SÍNDROME DE HIPERINMUNOGLOBULINEMIA E: REPORTE DE CASO CLÍNICO UNIVERSIDAD CATÓLICA DE CUENCA – ECUADOR, CARRERA DE MEDICINA MATRIZ

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María Vanessa Enderica Díaz
Dr. Andrés Santiago Bueno Castro
Dr. Pedro José Quizhpe Marín
Dr. Francisco Faicán Benenaula
Juan Pablo Uyaguari

Keywords

Hyperimmunoglobulinemia/, Immunoglobulin E/, pulmonary/, bronchiectasis

Abstract

Hyperimmunoglobulinemia E Syndrome (HIES) is a medical condition that can be sporadic or inherited. It consists of multiple overlapping primary immunodeficiencies and is characterized by a classic triad of elevated immunoglobulin E (IgE) levels, recurrent pneumonias, and skin abscesses. The prevalence of this pathology is 1/1,000,000 live births.

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