SPINAL ANAESTHESIA FOR INGUINAL HERNIA REPAIR IN A NEUROFIBROMATOSIS PATIENT WITH KYPHOSCOLIOSIS – A CASE REPORT
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Keywords
Neurofibromatosis, Spinal Anaesthesia, Kyphoscoliosis
Abstract
Neurofibromatosis type 1 (NF1) is an autosomal dominant neuroectodermal hereditary disorder, in which spinal skeletal deformities are one of the manifestations. Pectus carinatum, temporomandibular joint dysfunction and kyphoscoliosis can be seen with this genetic disorder which can lead to cardiorespiratory system problems and can cause difficulty in airway management. The clinical spectrum of this disorder is quite broad, characterized mainly by skin neurofibromata and café-au-lait spots. We report a case of 61 year old male with neurofibromatosis type 1 with kyphoscoliosis scheduled for left inguinal hernia repair. Patient was administered spinal anaesthesia at L4–L5 intervertebral space. Successful subarachnoid block was obtained and the surgery was performed successfully without any untoward complications.
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Dr. Harini Priyadarshini M. S
HOD & Senior Consultant, Department of Anaesthesia, K C General Hospital, Malleshwaram, Bengaluru, Karnataka, India.
Dr. Priyanka N. Maiya
Consultant Anaesthesiologist, Department of Anaesthesia, K C General Hospital, Malleshwaram, Bengaluru, Karnataka, India.
Dr. Srija P.
Consultant Anaesthesiologist, Department of Anaesthesia, K C General Hospital, Malleshwaram, Bengaluru, Karnataka, India.